Herbert Bonkovsky to Porphyrias
This is a "connection" page, showing publications Herbert Bonkovsky has written about Porphyrias.
Connection Strength
4.545
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Jaramillo-Calle DA, Solano JM, Rabinstein AA, Bonkovsky HL. Porphyria-induced posterior reversible encephalopathy syndrome and central nervous system dysfunction. Mol Genet Metab. 2019 11; 128(3):242-253.
Score: 0.684
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Bissell DM, Anderson KE, Bonkovsky HL. Porphyria. N Engl J Med. 2017 11 23; 377(21):2101.
Score: 0.598
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Besur S, Schmeltzer P, Bonkovsky HL. Acute Porphyrias. J Emerg Med. 2015 Sep; 49(3):305-12.
Score: 0.507
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Bonkovsky HL, Guo JT, Hou W, Li T, Narang T, Thapar M. Porphyrin and heme metabolism and the porphyrias. Compr Physiol. 2013 Jan; 3(1):365-401.
Score: 0.426
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Bonkovsky HL. Neurovisceral porphyrias: what a hematologist needs to know. Hematology Am Soc Hematol Educ Program. 2005; 24-30.
Score: 0.245
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Li P, Maitra D, Kuo N, Bonkovsky HL, Omary MB. Geographic prevalence variation and phenotype penetrance in porphyria: insights from a Chinese population database. Blood Adv. 2021 01 12; 5(1):12-15.
Score: 0.186
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Maitra D, Bragazzi Cunha J, Elenbaas JS, Bonkovsky HL, Shavit JA, Omary MB. Porphyrin-Induced Protein Oxidation and Aggregation as a Mechanism of Porphyria-Associated Cell Injury. Cell Mol Gastroenterol Hepatol. 2019; 8(4):535-548.
Score: 0.167
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Chen B, Whatley S, Badminton M, Aarsand AK, Anderson KE, Bissell DM, Bonkovsky HL, Cappellini MD, Floderus Y, Friesema ECH, Gouya L, Harper P, Kauppinen R, Loskove Y, Martásek P, Phillips JD, Puy H, Sandberg S, Schmitt C, To-Figueras J, Weiss Y, Yasuda M, Deybach JC, Desnick RJ. International Porphyria Molecular Diagnostic Collaborative: an evidence-based database of verified pathogenic and benign variants for the porphyrias. Genet Med. 2019 11; 21(11):2605-2613.
Score: 0.165
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Kalman DR, Bonkovsky HL. Management of acute attacks in the porphyrias. Clin Dermatol. 1998 Mar-Apr; 16(2):299-306.
Score: 0.152
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Bonkovsky HL, Barnard GF. Diagnosis of porphyric syndromes: a practical approach in the era of molecular biology. Semin Liver Dis. 1998; 18(1):57-65.
Score: 0.151
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Gou EW, Balwani M, Bissell DM, Bloomer JR, Bonkovsky HL, Desnick RJ, Naik H, Phillips JD, Singal AK, Wang B, Keel S, Anderson KE. Pitfalls in Erythrocyte Protoporphyrin Measurement for Diagnosis and Monitoring of Protoporphyrias. Clin Chem. 2015 Dec; 61(12):1453-6.
Score: 0.129
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Russo SM, Pepe JA, Cable EE, Lambrecht RW, Bonkovsky HL. Repression of ALA synthase by heme and zinc-mesoporphyrin in a chick embryo liver cell culture model of acute porphyria. Eur J Clin Invest. 1994 Jun; 24(6):406-15.
Score: 0.118
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Bonkovsky HL. Advances in understanding and treating 'the little imitator,' acute porphyria. Gastroenterology. 1993 Aug; 105(2):590-4.
Score: 0.111
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Bonkovsky HL, Healey JF, Lourie AN, Gerron GG. Intravenous heme-albumin in acute intermittent porphyria: evidence for repletion of hepatic hemoproteins and regulatory heme pools. Am J Gastroenterol. 1991 Aug; 86(8):1050-6.
Score: 0.097
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Tian Q, Li T, Hou W, Zheng J, Schrum LW, Bonkovsky HL. Lon peptidase 1 (LONP1)-dependent breakdown of mitochondrial 5-aminolevulinic acid synthase protein by heme in human liver cells. J Biol Chem. 2011 Jul 29; 286(30):26424-30.
Score: 0.096
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Bonkovsky HL. Iron and the liver. Am J Med Sci. 1991 Jan; 301(1):32-43.
Score: 0.093
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Bloomer JR, Bonkovsky HL. The porphyrias. Dis Mon. 1989 Jan; 35(1):1-54.
Score: 0.081
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Bonkovsky HL, Siao P, Roig Z, Hedley-Whyte ET, Flotte TJ. Case records of the Massachusetts General Hospital. Case 20-2008. A 57-year-old woman with abdominal pain and weakness after gastric bypass surgery. N Engl J Med. 2008 Jun 26; 358(26):2813-25.
Score: 0.078
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Zheng J, Tian Q, Hou W, Watts JA, Schrum LW, Bonkovsky HL. Tissue-specific expression of ALA synthase-1 and heme oxygenase-1 and their expression in livers of rats chronically exposed to ethanol. FEBS Lett. 2008 Jun 11; 582(13):1829-34.
Score: 0.077
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Bonkovsky HL, Sinclair PR, Bement WJ, Lambrecht RW, Sinclair JF. Role of cytochrome P-450 in porphyria caused by halogenated aromatic compounds. Ann N Y Acad Sci. 1987; 514:96-112.
Score: 0.070
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Sinclair PR, Sinclair JF, Bement WJ, Lambrecht RW, Bonkovsky HL. Induction of porphyria in cultured chick-embryo hepatocytes by halogenated aromatic compounds. IARC Sci Publ. 1986; (77):535-42.
Score: 0.066
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Bonkovsky HL, Schned AR. Fatal liver failure in protoporphyria. Synergism between ethanol excess and the genetic defect. Gastroenterology. 1986 Jan; 90(1):191-201.
Score: 0.066
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Elder GH, Urquhart AJ, De Salamanca RE, Munoz JJ, Bonkovsky HL. Immunoreactive uroporphyrinogen decarboxylase in the liver in porphyria cutanea tarda. Lancet. 1985 Aug 03; 2(8449):229-33.
Score: 0.064
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Lambrecht RW, Gildemeister OS, Pepe JA, Tortorelli KD, Williams A, Bonkovsky HL. Effects of antidepressants and benzodiazepine-type anxiolytic agents on hepatic porphyrin accumulation in primary cultures of chick embryo liver cells. J Pharmacol Exp Ther. 1999 Dec; 291(3):1150-5.
Score: 0.043
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Hahn M, Gildemeister OS, Krauss GL, Pepe JA, Lambrecht RW, Donohue S, Bonkovsky HL. Effects of new anticonvulsant medications on porphyrin synthesis in cultured liver cells: potential implications for patients with acute porphyria. Neurology. 1997 Jul; 49(1):97-106.
Score: 0.036
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Bonkovsky HL, Cable EE, Cable JW, Donohue SE, White EC, Greene YJ, Lambrecht RW, Srivastava KK, Arnold WN. Porphyrogenic properties of the terpenes camphor, pinene, and thujone (with a note on historic implications for absinthe and the illness of Vincent van Gogh). Biochem Pharmacol. 1992 Jun 09; 43(11):2359-68.
Score: 0.026
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Bonkovsky HL, Healey JF, Bement WJ, Sinclair PR, Sinclair JF, Shedlofsky SI. Effect of uroporphyrin on the spectral measurement of cytochrome P450. Biochem Pharmacol. 1984 Feb 01; 33(3):499-502.
Score: 0.014