The TREX1 double-stranded DNA degradation activity is defective in dominant mutations associated with autoimmune disease.
                             
                            
                            
                                
                            
                            
                                
                            
                            
                            
                                
                                    
                                            
    Lehtinen DA, Harvey S, Mulcahy MJ, Hollis T, Perrino FW. The TREX1 double-stranded DNA degradation activity is defective in dominant mutations associated with autoimmune disease. J Biol Chem. 2008 Nov 14; 283(46):31649-56.